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Familial ‘‘benign’’ pemphigus? Erythroderma and fatal outcome
dc.contributor.author | Tansini, Paula Baldissera | pt_BR |
dc.contributor.author | Boff, Ana Letícia | pt_BR |
dc.contributor.author | Weber, Magda Blessmann | pt_BR |
dc.contributor.author | Bonamigo, Renan Rangel | pt_BR |
dc.date.accessioned | 2020-07-23T03:40:33Z | pt_BR |
dc.date.issued | 2020 | pt_BR |
dc.identifier.issn | 0365-0596 | pt_BR |
dc.identifier.uri | http://hdl.handle.net/10183/212341 | pt_BR |
dc.description.abstract | Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual case of generalized Hailey-Hailey disease with erythroderma and fatal outcome. | en |
dc.format.mimetype | application/pdf | pt_BR |
dc.language.iso | eng | pt_BR |
dc.relation.ispartof | Anais brasileiros de dermatologia. Vol. 95, no. 1 (2020), p. 75-77 | pt_BR |
dc.rights | Open Access | en |
dc.subject | Pênfigo familiar benigno | pt_BR |
dc.subject | Pemphigus, benign familial | en |
dc.subject | Dermatitis, exfoliative | en |
dc.subject | Dermatite esfoliativa | pt_BR |
dc.subject | Skin diseases | en |
dc.subject | Relatos de casos | pt_BR |
dc.subject | Vesiculobullous | en |
dc.title | Familial ‘‘benign’’ pemphigus? Erythroderma and fatal outcome | pt_BR |
dc.type | Artigo de periódico | pt_BR |
dc.identifier.nrb | 001114856 | pt_BR |
dc.type.origin | Nacional | pt_BR |
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